Ferret and Pig Models of Cystic Fibrosis: Prospects and Promise for Gene Therapy-Reference-Cited by-同舟云学术

Ferret and Pig Models of Cystic Fibrosis: Prospects and Promise for Gene Therapy

Published:2015-03 Issue:1 Volume:26 Page:38-49
ISSN:2324-8637
Container-title:Human Gene Therapy Clinical Development
language:en
Short-container-title:Human Gene Therapy Clinical Development

Author:

Yan Ziying¹²,Stewart Zoe A.³,Sinn Patrick L.²⁴,Olsen John C.⁵,Hu Jim⁶,McCray Paul B.²⁴,Engelhardt John F.¹²⁷

Affiliation:

1. Department of Anatomy and Cell Biology, University of Iowa School of Medicine, Iowa City, IA 52242.

2. Center for Gene Therapy of Cystic Fibrosis, University of Iowa School of Medicine, Iowa City, IA 52242.

3. Department of Surgery, University of Iowa School of Medicine, Iowa City, IA 52242.

4. Department of Pediatrics, University of Iowa School of Medicine, Iowa City, IA 52242.

5. Cystic Fibrosis/Pulmonary Research and Treatment Center, Department of Medicine, University of North Carolina at Chapel Hill, Chapel Hill, NC 27599.

6. Department of Laboratory Medicine and Pathobiology, Hospital for Sick Children and University of Toronto, Toronto, ON M5G 0A4, Canada.

7. Department of Internal Medicine, University of Iowa School of Medicine, Iowa City, IA 52242.

Publisher

Mary Ann Liebert Inc

Subject

Genetics (clinical)

Link

http://www.liebertpub.com/doi/pdf/10.1089/humc.2014.154

Reference149 articles.

1. Identification of the Cystic Fibrosis Gene: Cloning and Characterization of Complementary DNA

2. Identification of the Cystic Fibrosis Gene: Chromosome Walking and Jumping

3. Identification of the Cystic Fibrosis Gene: Genetic Analysis

4. Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells

5. Mechanism of direct bicarbonate transport by the CFTR anion channel

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