Conformational and Temperature-sensitive Stability Defects of the ΔF508 Cystic Fibrosis Transmembrane Conductance Regulator in Post-endoplasmic Reticulum Compartments-Reference-Cited by-同舟云学术

Conformational and Temperature-sensitive Stability Defects of the ΔF508 Cystic Fibrosis Transmembrane Conductance Regulator in Post-endoplasmic Reticulum Compartments

Published:2001-03 Issue:12 Volume:276 Page:8942-8950
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Sharma Manu,Benharouga Mohamed,Hu Wei,Lukacs Gergely L.

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference47 articles.

1. Identification of the Cystic Fibrosis Gene: Genetic Analysis

2. Identification of the Cystic Fibrosis Gene: Chromosome Walking and Jumping

3. Identification of the Cystic Fibrosis Gene: Cloning and Characterization of Complementary DNA

4. Conformational maturation of CFTR but not its mutant counterpart (delta F508) occurs in the endoplasmic reticulum and requires ATP.

5. Intracellular turnover of cystic fibrosis transmembrane conductance regulator. Inefficient processing and rapid degradation of wild-type and mutant proteins.

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