Cholesterol Is Sequestered in the Brains of Mice with Niemann-Pick Type C Disease but Turnover Is Increased-Reference-Cited by-同舟云学术

Cholesterol Is Sequestered in the Brains of Mice with Niemann-Pick Type C Disease but Turnover Is Increased

Published:2000-12 Issue:12 Volume:59 Page:1106-1117
ISSN:0022-3069
Container-title:Journal of Neuropathology & Experimental Neurology
language:en
Short-container-title:J Neuropathol Exp Neurol

Author:

Xie Chonglun,Burns Dennis K.,Turley Stephen D.,Dietschy John M.

Publisher

Oxford University Press (OUP)

Subject

Cellular and Molecular Neuroscience,Neurology (clinical),Neurology,General Medicine,Pathology and Forensic Medicine

Link

http://academic.oup.com/jnen/article-pdf/59/12/1106/8132878/59-12-1106.pdf

Reference68 articles.

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2. Cerebellar degeneration in the Niemann-Pick type C mouse;Higashi;Acta Neuropathol,1993

3. Pentchev PG Vanier MT Suzuki K Patterson MC . Niemann-Pick disease type C: A cellular cholesterol lipidosis. In: Scriver CR Beaudet AL Sly WS , eds. The metabolic and molecular bases of inherited diseases, 7th Ed. New York: McGraw-Hill, 1995:; 2625–39

4. Nova Scotia Niemann-Pick Disease (Type D): Clinical Study of 20 Cases

5. A genetic storage disorder in BALB/C mice with a metabolic block in esterification of exogenous cholesterol;Pentchev;J Biol Chem,1984

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