Acid ceramidase improves mitochondrial function and oxidative stress in Niemann-Pick type C disease by repressing STARD1 expression and mitochondrial cholesterol accumulation-Reference-Cited by-同舟云学术

Acid ceramidase improves mitochondrial function and oxidative stress in Niemann-Pick type C disease by repressing STARD1 expression and mitochondrial cholesterol accumulation

Published:2021-09 Issue: Volume:45 Page:102052
ISSN:2213-2317
Container-title:Redox Biology
language:en
Short-container-title:Redox Biology

Author:

Torres Sandra,Solsona-Vilarrasa Estel,Nuñez Susana,Matías Nuria,Insausti-Urkia Naroa^ORCID,Castro Fernanda,Casasempere Mireia,Fabriás Gemma,Casas Josefina,Enrich Carlos,Fernández-Checa José C.,Garcia-Ruiz Carmen

Funder

NIAAA

Publisher

Elsevier BV

Subject

Organic Chemistry,Biochemistry,Clinical Biochemistry

Reference49 articles.

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2. Complex lipid trafficking in Niemann-Pick disease type C;Vanier;J. Inherit. Metab. Dis.,2015

3. Structure of N-terminal domain of NPC1 reveals distinct subdomains for binding and transfer of cholesterol;Kwon;Cell,2009

4. Lysosome and endoplasmic reticulum quality control pathways in Niemann-Pick type C disease;Schultz;Brain Res.,2016

5. Cholesterol accumulation and liver cell death in mice with Niemann-Pick type C disease;Beltroy;Hepatology,2005

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