Transgenic Human α-Hemoglobin Stabilizing Protein Could Partially Relieve βIVS-2-654-Thalassemia Syndrome in Model Mice-Reference-Cited by-同舟云学术

Transgenic Human α-Hemoglobin Stabilizing Protein Could Partially Relieve βIVS-2-654-Thalassemia Syndrome in Model Mice

Published:2010-02 Issue:2 Volume:21 Page:149-156
ISSN:1043-0342
Container-title:Human Gene Therapy
language:en
Short-container-title:Human Gene Therapy

Author:

Wang Baobin¹,Fang Yudan¹²,Guo Xinbing¹²,Ren Zhaorui¹,Zhang Jingzhi¹²

Affiliation:

1. Shanghai Institute of Medical Genetics, Shanghai Children's Hospital, Shanghai Jiao Tong University School of Medicine, Shanghai 200040, People's Republic of China.

2. Key Laboratory of Embryonic Molecular Biology, Ministry of Health, Shanghai 200040, People's Republic of China; and Laboratory of Embryonic and Reproductive Engineering, Shanghai 200040, People's Republic of China.

Publisher

Mary Ann Liebert Inc

Subject

Genetics,Molecular Biology,Molecular Medicine

Link

http://www.liebertpub.com/doi/pdf/10.1089/hum.2009.132

Reference21 articles.

1. Molecular Analysis of Alpha Hemoglobin Stabilizing Protein (AHSP) in Caucasian Patients with different Beta-Thalassemia Phenotypes.

2. Molecular Mechanism of AHSP-Mediated Stabilization of α-Hemoglobin

3. Structure of oxidized α-haemoglobin bound to AHSP reveals a protective mechanism for haem

4. GATA-1 and Oct-1 Are Required for Expression of the Human α-Hemoglobin-stabilizing Protein Gene

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