Congenitally Unguarded Tricuspid Orifice with Coexistent Pulmonary Atresia

Abstract

A rare malformation of the tricuspid valve is described in which neither valvular tissue nor papillary muscles were formed, while a tricuspid orifice was present. The case involved a cyanotic newborn female infant in whom pulmonary valvular atresia was also present. The functional, clinical, and angiocardiographic manifestations were similar to those that may be observed either in tricuspid atresia or in pulmonary atresia with intact ventricular septum. As far as we are aware, the literature contains only one other case which bears some similarity but is not identical to the one herein reported.