Developmental dysplasia of the hip in an epidermolysis bullosa patient; how to deal with surgical difficulties: A case report

Abstract

Epidermolysis bullosa (EB) is defined as a separation of the dermoepidermal junctions resulting in an increased risk of infection and the formation of fibrous tissue. We are presenting a case of a 22-month-old girl with developmental dysplasia of the left hip and EB. The patient was operated on, with the left hip open reduction, acetabuloplasty and hip spica application. For a safe surgery on EB patients, pre-operative anesthesia assessment is necessary to ensure proper neck movement and examine the mouth and airway for the presence of blisters. Certain intraoperative measures should be taken, like gentle handling of the patient to reduce the events of blistering and scarring. Avoiding all adherent dressings, tapes, and stickers, using non-adhesive dressings and applying a good cotton padding for patients, are crucial steps in such cases to achieve good results. Surgery for this patient went smoothly without acute complications. In this report, we hope to provide helpful information on the surgical management of such patients.