Redox homeostasis is compromised in vivo by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in rat cerebral cortex and liver
Author:
Publisher
Informa UK Limited
Subject
General Medicine,Biochemistry
Link
http://www.tandfonline.com/doi/pdf/10.3109/10715762.2013.853876
Reference47 articles.
1. Evaluation of Urinary Acylglycines by Electrospray Tandem Mass Spectrometry in Mitochondrial Energy Metabolism Defects and Organic Acidurias
2. The contribution of protein catabolism to metabolic decompensation in 3-hydroxy-3-methylglutaric aciduria
3. Lethal hypoglycemia in a child with a deficiency of 3-hydroxy-3-methylglutarylcoenzyme A lyase
4. 3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: A review
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