Affiliation:
1. Department of Medicine, University of Ceylon.
Abstract
Abstract
1. A case of congenital afibrinogenemia of a Sinhalese boy of 22 years is reported.
2. The main features of the reported cases are reviewed.
3. The principal features of this case are total absence of fibrinogen in the blood, complete non-coagulability of blood, history of several episodes of hemorrhage dating from infancy, low erythrocyte sedimentation rate, cosanguinity of the parents and the occurrence of spontaneous hemoperitoneum from which he recovered after operation.
4. Treatment consists of blood or fibrinogen transfusion.
Publisher
American Society of Hematology
Subject
Cell Biology,Hematology,Immunology,Biochemistry
Cited by
16 articles.
订阅此论文施引文献
订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献
1. Healed retinal vasculitis in a child with hypofibrinogenemia;Indian Journal of Ophthalmology - Case Reports;2024-04
2. Congenital Fibrinogen Abnormalities;Annals of the New York Academy of Sciences;1983-06
3. Diagnostische und therapeutische Probleme bei congenitaler Afibrinogenämie;Blut Zeitschrift für die Gesamte Blutforschung;1971-04
4. Irregular Blood Coagulation;Blood Clotting Enzymology;1967
5. Genetics of human blood coagulation.;Journal of Medical Genetics;1965-12-01