Therapeutic effects of the mitochondrial ROS-redox modulator KH176 in a mammalian model of Leigh Disease-Reference-Cited by-同舟云学术

Therapeutic effects of the mitochondrial ROS-redox modulator KH176 in a mammalian model of Leigh Disease

Published:2017-09-15 Issue:1 Volume:7 Page:
ISSN:2045-2322
Container-title:Scientific Reports
language:en
Short-container-title:Sci Rep

Author:

de Haas Ria,Das Devashish^ORCID,Garanto Alejandro,Renkema Herma G.,Greupink Rick,van den Broek Petra,Pertijs Jeanne,Collin Rob W. J.,Willems Peter,Beyrath Julien,Heerschap Arend,Russel Frans G.,Smeitink Jan A.

Publisher

Springer Science and Business Media LLC

Subject

Multidisciplinary

Link

http://www.nature.com/articles/s41598-017-09417-5.pdf

Reference70 articles.

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4. Jonckheere, A. I. et al. A complex V ATP5A1 defect causes fatal neonatal mitochondrial encephalopathy. Brain: a journal of neurology 136, 1544–1554, doi: 10.1093/brain/awt086 (2013).

5. Nouws, J., Nijtmans, L. G., Smeitink, J. A. & Vogel, R. O. Assembly factors as a new class of disease genes for mitochondrial complex I deficiency: cause, pathology and treatment options. Brain: a journal of neurology 135, 12–22, doi: 10.1093/brain/awr261 (2012).

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