Defective function of α-ketoglutarate dehydrogenase exacerbates mitochondrial ATP deficits during complex I deficiency-Reference-Cited by-同舟云学术

Defective function of α-ketoglutarate dehydrogenase exacerbates mitochondrial ATP deficits during complex I deficiency

Published:2023-11 Issue: Volume:67 Page:102932
ISSN:2213-2317
Container-title:Redox Biology
language:en
Short-container-title:Redox Biology

Author:

Piroli Gerardo G.,Manuel Allison M.,McCain Richard S.,Smith Holland H.,Ozohanics Oliver,Mellid Sara,Cox J. Hunter,Cotham William E.,Walla Michael D.,Cascón Alberto,Ambrus Attila,Frizzell Norma

Funder

Hungarian Scientific Research Fund

National Institutes of Health

University of South Carolina

Publisher

Elsevier BV

Subject

Organic Chemistry,Biochemistry,Clinical Biochemistry

Reference82 articles.

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3. Ndufs4 related Leigh syndrome: a case report and review of the literature;Ortigoza-Escobar;Mitochondrion,2016

4. Mice with mitochondrial complex I deficiency develop a fatal encephalomyopathy;Kruse;Cell Metabol.,2008

5. Complex I deficiency due to loss of Ndufs4 in the brain results in progressive encephalopathy resembling Leigh syndrome;Quintana;Proc. Natl. Acad. Sci. U.S.A.,2010

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