Direct Determination of the Substrate Specificity of the α-Active Site in Heterodimeric β-Hexosaminidase A-Reference-Cited by-同舟云学术

Direct Determination of the Substrate Specificity of the α-Active Site in Heterodimeric β-Hexosaminidase A

Published:1996-01-01 Issue:13 Volume:35 Page:3963-3969
ISSN:0006-2960
Container-title:Biochemistry
language:en
Short-container-title:Biochemistry

Author:

Hou Yongmin¹,Tse Roderick¹,Mahuran Don J.¹

Affiliation:

1. Research Institute, Hospital for Sick Children, Toronto, Ontario M5G 1X8, Canada, and Department of Clinical Biochemistry, University of Toronto, Toronto, Ontario M5G 2C4, Canada

Publisher

American Chemical Society (ACS)

Subject

Biochemistry

Link

https://pubs.acs.org/doi/pdf/10.1021/bi9524575

Reference43 articles.

1. Correction of human mucopolysaccharidosis type-VI fibroblasts with recombinant N-acetylgalactosamine-4-sulphatase

2. Synthesis of and its use in classification of GM2 gangliosidosis genotypes

3. A difference in the specificities of human liver N-acetyl-β-hexosaminidases A and B detected by their activities towards glycosaminoglycan oligosaccharides

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