Lipid Status and Long-Chain Polyunsaturated Fatty Acid Concentrations in Adults and Adolescents with Phenylketonuria on Phenylalanine-Restricted Diet
Author:
Affiliation:
1. ; Children's Hospital of Los Angeles, Division of Medical Genetics; University of Southern California School of Medicine; Los Angeles California
2. ; Kennedy Krieger Institute; Baltimore Maryland USA
Publisher
Wiley
Subject
Genetics (clinical),Genetics
Link
http://onlinelibrary.wiley.com/wol1/doi/10.1023/A:1015142001578/fullpdf
Reference13 articles.
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2. Significantly reduced docosahexaenoic and docosapentaenoic acid concentrations in erythrocyte membranes from schizophrenic patients compared with a carefully matched control group;Assies;Biol Psychiatry,2001
3. Reduced plasma C-20 and C-22 polyunsaturated fatty acids in children with phenylketonuria during dietary intervention;Galli;J Pediatr,1991
4. Impaired arachidonic (20:4n - 6) and docosahexaenoic (22:6n - 3) acid synthesis by phenylalanine metabolites as etiological factors in the neuropathology of phenylketonuria;Infante;Mol Genet Metab,2001
5. Direct transesterification of plasma fatty acids for the diagnosis of essential fatty acid deficiency in cystic fibrosis;Lepage;J Lipid Res,1989
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