On the mechanism of gating defects caused by the R117H mutation in cystic fibrosis transmembrane conductance regulator-Reference-Cited by-同舟云学术

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On the mechanism of gating defects caused by the R117H mutation in cystic fibrosis transmembrane conductance regulator

Published:2016-03-23 Issue:12 Volume:594 Page:3227-3244
ISSN:0022-3751
Container-title:The Journal of Physiology
language:en
Short-container-title:J Physiol

Author:

Yu Ying-Chun¹²,Sohma Yoshiro¹³,Hwang Tzyh-Chang¹²

Affiliation:

1. Dalton Cardiovascular Research Center; University of Missouri-Columbia; MO 65211 USA

2. Department of Medical Pharmacology and Physiology; University of Missouri-Columbia; MO 65211 USA

3. Department of Pharmacology; Keio University School of Medicine; Shinjuku Tokyo 160-8582 Japan

Publisher

Wiley

Subject

Physiology

Reference50 articles.

1. Dual roles of the sixth transmembrane segment of the CFTR chloride channel in gating and permeation;Bai;J Gen Physiol,2010

2. CFTR gating I: characterization of the ATP-dependent gating of a phosphorylation-independent CFTR channel (ΔR-CFTR);Bompadre;J Gen Physiol,2005

3. CFTR gating II: effects of nucleotide binding on the stability of open states;Bompadre;J Gen Physiol,2005

4. Mechanism of G551D-CFTR (cystic fibrosis transmembrane conductance regulator) potentiation by a high affinity ATP analog;Bompadre;J Biol Chem,2008

5. G551D and G1349D, two CF-associated mutations in the signature sequences of CFTR, exhibit distinct gating defects;Bompadre;J Gen Physiol,2007

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