The Cystic Fibrosis-causing Mutation ΔF508 Affects Multiple Steps in Cystic Fibrosis Transmembrane Conductance Regulator Biogenesis-Reference-Cited by-同舟云学术

The Cystic Fibrosis-causing Mutation ΔF508 Affects Multiple Steps in Cystic Fibrosis Transmembrane Conductance Regulator Biogenesis

Published:2010-11 Issue:46 Volume:285 Page:35825-35835
ISSN:0021-9258
Container-title:Journal of Biological Chemistry
language:en
Short-container-title:Journal of Biological Chemistry

Author:

Thibodeau Patrick H.,Richardson John M.,Wang Wei,Millen Linda,Watson Jarod,Mendoza Juan L.,Du Kai,Fischman Sharon,Senderowitz Hanoch,Lukacs Gergely L.,Kirk Kevin,Thomas Philip J.

Publisher

Elsevier BV

Subject

Cell Biology,Molecular Biology,Biochemistry

Reference44 articles.

1. Energetics of membrane protein folding and stability

2. Coordinated Nonvectorial Folding in a Newly Synthesized Multidomain Protein

3. Cotranslational Folding Promotes β-Helix Formation and Avoids Aggregation In Vivo

4. Identification of the Cystic Fibrosis Gene: Cloning and Characterization of Complementary DNA

5. Structure of nucleotide-binding domain 1 of the cystic fibrosis transmembrane conductance regulator

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