Cystinosis: Therapy adherence and metabolic monitoring in patients treated with immediate-release cysteamine
Author:
Funder
Orphan Europe
Horizon Pharmaceuticals
University of Muenster
Publisher
Elsevier BV
Subject
Endocrinology,Genetics,Molecular Biology
Reference13 articles.
1. Cystinose;Harms,2014
2. Cystinotic fibroblasts accumulate cystine from intracellular protein degradation;Thoene;Proc. Natl. Acad. Sci. U. S. A.,1977
3. Increased cystine in leukocytes from individuals homozygous and heterozygous for cystinosis;Schneider;Science,1967
4. Lysosomal cystine storage augments apoptosis in cultured human fibroblasts and renal tubular epithelial cells;Park;J. Am. Soc. Nephrol.,2002
5. Cystinosis;Gahl;N. Engl. J. Med.,2002
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