Kinetic Instability of the Serpin Z α1-Antitrypsin Promotes Aggregation
Author:
Publisher
Elsevier BV
Subject
Molecular Biology,Structural Biology
Reference46 articles.
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5. Serum alpha 1-antitrypsin deficiency associated with the common S-type (Glu264–Val) mutation results from intracellular degradation of alpha 1-antitrypsin prior to secretion;Curiel;J. Biol. Chem.,1989
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