Protein and lipid damage in maple syrup urine disease patients: l ‐carnitine effect-Reference-Cited by-同舟云学术

Protein and lipid damage in maple syrup urine disease patients: l ‐carnitine effect

Published:2012-11-05 Issue:1 Volume:31 Page:21-24
ISSN:0736-5748
Container-title:International Journal of Developmental Neuroscience
language:en
Short-container-title:Int. j. dev. neurosci.

Author:

Mescka Caroline Paula¹,Wayhs Carlos Alberto Yasin²,Vanzin Camila Simioni¹,Biancini Giovana Brondani¹,Guerreiro Gilian³,Manfredini Vanusa⁴,Souza Carolina³,Wajner Moacir³¹,Dutra‐filho Carlos Severo¹,Vargas Carmen Regla³¹²

Affiliation:

1. Programa de Pós‐Graduação em CB:Bioquímica e Departamento de BioquímicaUFRGSRua Ramiro Barcelos, 260090035‐000Porto AlegreRSBrazil

2. Programa de Pós‐Graduação em Ciências FarmacêuticasUFRGSAv. Ipiranga, 275290610‐000Porto AlegreRSBrazil

3. Serviço de Genética MédicaHCPAUFRGSRua Ramiro Barcelos, 235090035‐903Porto AlegreRSBrazil

4. Universidade Federal do PampaBR 472, Km 585, Caixa Postal 11897500‐970UruguaianaRSBrazil

Funder

Fundação de Amparo à Pesquisa do Estado do Rio Grande do Sul

Conselho Nacional de Desenvolvimento Científico e Tecnológico

Publisher

Wiley

Subject

Developmental Biology,Developmental Neuroscience

Link

https://onlinelibrary.wiley.com/doi/pdf/10.1016/j.ijdevneu.2012.10.109

Reference23 articles.

1. Evidence that oxidative stress is increased in plasma from patients with maple syrup urine disease

2. Oxidative stress in plasma from maple syrup urine disease patients during treatment

3. Induction of oxidative stress in rat brain by the metabolites accumulating in maple syrup urine disease

4. Rapid diagnosis of MCAD deficiency: quantitative analysis of octanoylcarnitine and other acylcarnitines in newborn blood spots by tandem mass spectrometry;Chace D.H.;Clinical Chemistry,1997

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