Memantine Improves Memory and Neurochemical Damage in a Model of Maple Syrup Urine Disease

Author:

Lemos Isabela da SilvaORCID,Torres Carolina AntunesORCID,Alano Carolina GiassiORCID,Matiola Rafaela TezzaORCID,de Figueiredo Seldenreich RejaneORCID,Padilha Alex Paulo ZeferinoORCID,De Pieri EllenORCID,Effting Pauline SouzaORCID,Machado-De-Ávila Ricardo AndrezORCID,Réus Gislaine ZilliORCID,Leipnitz GuilhianORCID,Streck Emilio LuizORCID

Funder

Coordenação de Aperfeiçoamento de Pessoal de Nível Superior

Conselho Nacional de Desenvolvimento Científico e Tecnológico

Fundação de Amparo à Pesquisa e Inovação do Estado de Santa Catarina

Publisher

Springer Science and Business Media LLC

Subject

Cellular and Molecular Neuroscience,General Medicine,Biochemistry

Reference83 articles.

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2. Dancis J, Levitz M, Westall RG (1960) Maple syrup urine disease: branched-chain keto-aciduria. Pediatrics 25:72–79

3. Strauss KA, Morton DH (2003) Branched-chain ketoacyl dehydrogenase deficiency: maple syrup disease. Curr Treat Options Neurol 5:329–341

4. Strauss KA, Carson VJ, Soltys K, Young ME, Bowser LE, Puffenberger EG, Brigatti KW, Williams KB, Robinson DL, Hendrickson C, Beiler K, Taylor CM, Haas-Givler B, Chopko S, Hailey J, Muelly ER, Shellmer DA, Radcliff Z, Rodrigues A, Loeven K, Heaps AD, Mazariegos GV, Morton DH (2020) Branched-chain α-ketoacid dehydrogenase deficiency (maple syrup urine disease): treatment, biomarkers, and outcomes. Mol Genet Metab 129:193–206

5. Sánchez SJ, Visus A, Minana F (2010) Enfermidades de orina de jarabe arce. In: Sanjurjo PBA (ed) Diagnóstico y tratamiento de las enfermedades metabólicas hereditárias 3edn. Eddiciones Ergon, Madrid, p 1332

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