Characterization of 6-hexadecanoylamino-4-methylumbelliferyl-β-d-galactopyranoside as fluorogenic substrate of galactocerebrosidase for the diagnosis of Krabbe disease-Reference-Cited by-同舟云学术

Characterization of 6-hexadecanoylamino-4-methylumbelliferyl-β-d-galactopyranoside as fluorogenic substrate of galactocerebrosidase for the diagnosis of Krabbe disease

Published:1992-01 Issue:1-2 Volume:205 Page:87-96
ISSN:0009-8981
Container-title:Clinica Chimica Acta
language:en
Short-container-title:Clinica Chimica Acta

Author:

Wiederschain German,Srinivasa Raghavan,Kolodny Edwin

Publisher

Elsevier BV

Subject

Biochemistry, medical,Clinical Biochemistry,Biochemistry,General Medicine

Reference23 articles.

1. Galactosylceramide lipidosis: globoid cell leukodystrophy (Krabby disease;Suzuki,1989

2. Use of leukocytes in diagnosis of Krabbe disease and detection of carriers;Svennerholm;Clin Chim Acta,1981

3. The use of galactosylceramides with uniform fatty acids as substrates in the diagnosis and carrier detection of Krabbe disease;Mnsson;Clin Chim Acta,1982

4. Spectrophotometric and fluorimetruc assays of galactocerebrosidase activity, their use in the diagnosis of Krabber disease;Besley;Clin Chim Acta,1981

5. The use of the fluorescntly labelled cerebroside as a substrate for galactosylceramidase from human skin fibroblasts;Semenyuk;Biokhimiya,1984

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