Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice
Author:
Publisher
Elsevier BV
Subject
Cell Biology,Endocrinology,Biochemistry
Reference65 articles.
1. β-Galactosidase deficiency (β-galactosidosis): GM1 gangliosidosis and Morquio B disease;Suzuki,1995
2. Generalized CNS disease and massive GM1-ganglioside accumulation in mice defective in lysosomal acid beta-galactosidase;Hahn;Hum. Mol. Genet.,1997
3. N-Butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis;Kasperzyk;J. Neurochem.,2004
4. Cell-mediated delivery systems;Dobrenis,2004
5. Expression of human beta-hexosaminidase alpha-subunit gene (the gene defect of Tay-Sachs disease) in mouse brains upon engraftment of transduced progenitor cells;Lacorazza;Nat. Med.,1996
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