Cln6 mutants associated with neuronal ceroid lipofuscinosis are degraded in a proteasome-dependent manner
Author:
Affiliation:
1. Mount Sinai School of Medicine, Department of Microbiology, One Gustave L. Levy Place, Box 1124, New York, NY 10029, U.S.A.
2. Whitehead Institute for Biomedical Research, Nine Cambridge Center, Cambridge, MA 02142-1479, U.S.A.
Abstract
Publisher
Portland Press Ltd.
Subject
Cell Biology,Molecular Biology,Biochemistry,Biophysics
Link
https://portlandpress.com/bioscirep/article-pdf/29/3/173/473236/bsr0290173.pdf
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4. Clinico-pathological variability in the childhood neuronal ceroid-lipofuscinoses and new observations on glycoprotein abnormalities;Wisniewski;Am. J. Med. Genet. Suppl.,1988
5. Brain lysosomal hydrolases in neuronal ceroid-lipofuscinoses;Prasad;Mol. Chem. Neuropathol.,1996
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