Nutritional management of patients with urea cycle disorders

Author:

Singh R. H.

Publisher

Wiley

Subject

Genetics(clinical),Genetics

Reference25 articles.

1. Acosta PB, Yannicelli S (2001) Protocol 24—Urea cycle disorders. The Ross Metabolic Formula System Nutrition Support Protocols, 4th edn. Columbus: Ross Products Division, 429.

2. Acosta PB, Yannicelli S, Ryan AS, et al (2005) Nutritional therapy improves growth and protein status of children with a urea cycle enzyme defect. Mol Genet Metab 86(4): 448-55.

3. Anonymous (2006) Newborn screening: toward a uniform screening panel and system. Genet Med 8(Supplement 1): 1S-52S.

4. Batshaw ML, MacArthur RB, Tuchman M (2001) Alternative pathway therapy for urea cycle disorders: twenty years later. J Pediatr 138(1 Supplement):S46–S54.

5. Berry GT, Steiner RD (2001) Long-term management of patients with urea cycle disorders. J Pediatr 138(1 Supplement): S56–S60.

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