Lessons from Knockout Mice. I: Phenotypes of Mice with Peroxisome Biogenesis Disorders
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Springer US
Link
http://link.springer.com/content/pdf/10.1007/978-1-4419-9072-3_16
Reference25 articles.
1. Baes, M., Dewerchin, M., Janssen, A., Collen, D., Carmeliet, P., 2002a, Generation of Pex5- IoxP mice allowing the conditional elimination of peroxisomes. Genesis 32: 177–178.
2. Baes, M., Gressens, P., Baumgart, E., Carmeliet, P., Casteels, M., Fransen, M., Evrard, P., Fahimi, D., Declercq, P.E., Collen, D., Van Veldhoven, P.P., Mannaerts, G.P. (1997). A mouse model for Zellweger syndrome. Nat. Genet. 17: 49–57.
3. Baes, M., Gressens, P., Huyghe, S., De Nys, K., Qi, C, Jia, Y., Mannaerts, G.P., Evrard, P., Van Veldhoven, P.P., Declercq, P.E., Reddy, J.K., 2002b. The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal ß-oxidation. J. Neuropath. Exp. Neur. 61: 368–374.
4. Baes, M., Huyghe, S., Carmeliet, P., Declercq, P.E., Collen, D., Mannaerts, G.P., Van Veldhoven, P.P., 2000, Inactivation of the peroxisomal multifunctional protein-2 in mice impedes the degradation of not only 2-methyl branched fatty acids and bile acid intermediates but also of very long chain fatty acids. J. Biol. Chem. 275: 16329–16336.
5. Baumgart, E., Vanhorebeek, I., Grabenbauer, M., Borgers, M., Declercq, P.E., Fahimi, H.D., Baes.M.. 2001, Mitochondrial alterations caused by defective peroxisomal biogenesis in a mouse model for Zellweger syndrome (Pex5 knockout mouse). Am. J. Patholog. 159: 1477–1494.
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