Primary Angiosarcoma of the Heart. A Case Report and Review of the English Literature

Abstract

Primary angiosarcoma of the heart is a rare tumor. In view of its variable clinical picture, the diagnosis is delayed and often difficult to establish without an open biopsy. In the majority of cases the tumor originates from the right atrium, metasta sizes early to distant sites, and carries a rapidly fatal outcome. The clinicopath ologic features and the methods of diagnosis for this highly malignant neoplasm are reviewed and a new case is reported.