Lipodystrophia Centrifugalis Abdominalis Infantilis

Abstract

Background: Lipodystrophia centrifugalis abdominalis infantilis (LCAI) is an uncommon dermatological condition characterized by a centrifugally expanding area of lipoatrophy involving the lower abdominal area and is frequently associated with inguinal lymphadenopathy. The average age of onset is 4 years and female individuals from Japan, China, and Korea are affected more often. Objectives: To report the first case of LCAI in a Vietnamese patient. Methods: A complete clinical assessment was done and a biopsy from the affected area was performed. Results: There was an atrophic, slightly hyperpigmented patch at the lower abdomen with prominent underlying vasculature. Inguinal lymphadenopathy was noted on the ipsilateral side. A biopsy showed a lobular panniculitis with fat necrosis and lymphohistiocytic infiltrate with scattered plasma cells and multinucleated giant cells. Conclusion: To our knowledge, this is the first reported case of LCAI in a Vietnamese patient.