Intracranial hypertension as the first manifestation of primary Sjögren’s syndrome

Abstract

Background: Central nervous system involvement with primary Sjögren’s syndrome (pSS) is rare, and often undiagnosed. Sjögren’s syndrome and concomitant intracranial hypertension is a very rare event. Case: We describe a patient with pSS who presented with intracranial hypertension as the initial symptom of the disease. Conclusion: This is the first case report of a patient with pSS that presented with intracranial hypertension only.