Pulmonary Artery Aneurysm Due to Severe Congenital Pulmonic Stenosis

Abstract

Although dilatation of the pulmonary artery (PA) is characteristic of pulmonic valve stenosis (PVS), the occurrence of a PA aneurysm in association with PVS is very rare. The authors describe a patient with severe, dome-shaped PVS who developed a 6.5 cm pulmonary trunk aneurysm. Long-term follow-up after surgical valvotomy demonstrated that the size of the aneurysm remained unchanged. Pertinent literature and implications on the natural history and management of these aneurysms are discussed.