Keratoderma Hereditarium Mutilans (Vohwinkel's Syndrome) Associated with Sensorineural Deafness in an HIV Positive Man: A Case Report

Abstract

Keratoderma hereditarium mutilans (KHM) or Vohwinkel's syndrome is a rare cutaneous disorder, characterized by thickening of palms and soles and by ainhum-like constrictions of the fingers and toes. KHM is usually inherited as an autosomal dominant disease, but a recessive type has occasionally been described.