Successful Medical-Surgical Management of Intracardiac Thrombosis and Pulmonary Pseudoaneurysms in an Adolescent With Hughes-Stovin Syndrome-Reference-Cited by-同舟云学术

Successful Medical-Surgical Management of Intracardiac Thrombosis and Pulmonary Pseudoaneurysms in an Adolescent With Hughes-Stovin Syndrome

Published:2023-01 Issue: Volume:11 Page:232470962311666
ISSN:2324-7096
Container-title:Journal of Investigative Medicine High Impact Case Reports
language:en
Short-container-title:Journal of Investigative Medicine High Impact Case Reports

Author:

Villacis-Nunez D. Sofia¹²^ORCID,West Zachary²³,Khan Adil Y.²³,Rodriguez Fred²⁴,Shane Andi L.²⁵,Rytting Heather⁶,Shashidharan Subhadra²⁷,Clifton Matthew S.²⁸,Woods Gary²⁹,Clabby Martha²⁴,Prahalad Sampath¹²¹⁰

Affiliation:

1. Division of Pediatric Rheumatology, Department of Pediatrics, Emory University School of Medicine, Atlanta, GA, USA

2. Children’s Healthcare of Atlanta, Atlanta, GA, USA

3. Division of Pediatric Hospital Medicine, Department of Pediatrics, Emory University School of Medicine, Atlanta, GA, USA

4. Sibley Heart Center, Atlanta, GA, USA

5. Division of Pediatric Infectious Diseases, Department of Pediatrics, Emory University School of Medicine, Atlanta, GA, USA

6. Department of Pathology, Children’s Healthcare of Atlanta, Atlanta, GA, USA

7. Department of Congenital Cardiac Surgery, Emory University School of Medicine, Atlanta, GA, USA

8. Department of Surgery, Emory University School of Medicine, Atlanta, GA, USA

9. Department of Pediatrics, Emory University School of Medicine, Atlanta, GA, USA

10. Department of Human Genetics, Emory University School of Medicine, Atlanta, GA, USA

Abstract

We present an adolescent male with a single intracardiac mass and pulmonary emboli, complicated by peripheral venous thrombosis and subsequent development of pulmonary pseudoaneurysms, leading to diagnosis of Hughes-Stovin syndrome. Remission was achieved with cyclophosphamide, corticosteroids, and pseudoaneurysm resection and maintained with infliximab and methotrexate.

Publisher

SAGE Publications

Subject

Safety Research,Safety, Risk, Reliability and Quality,Epidemiology

Link

http://journals.sagepub.com/doi/pdf/10.1177/23247096231166672

Reference7 articles.

1. Hughes-Stovin Syndrome

2. Intracardiac Thrombus in Behçet's Disease

3. A critical analysis of 57 cases of Hughes-Stovin syndrome (HSS). A report by the HSS International Study Group (HSSISG)

4. Diagnostic/classification criteria in pediatric Behçet’s disease

5. Consensus classification criteria for paediatric Behçet's disease from a prospective observational cohort: PEDBD