Repair of Isolated Atrial Inversion with Venous Return Abnormality

Abstract

A 33-year-old woman was found to have atrial inversion (atrioventricular discordance), right-hand ventricular morphology, ventriculoarterial concordance associated with a primum atrial septal defect, and abnormal systemic and pulmonary venous return. The pulmonary veins, inferior vena cava, and left superior vena cava drained into the left-sided morphologically right atrium. Only the right superior vena cava drained into the right-sided morphologically left atrium. Intraatrial baffle repair was performed successfully.