Primary cardiac synovial sarcoma. A rare tumor with poor prognosis

Abstract

Synovial sarcoma comprises approximately 10% of all soft tissue tumors. Primary cardiac synovial sarcoma is exceedingly rare and accounts for <1% of all primary cardiac tumors. These tumors are highly aggressive with survival <1 year, even with surgery, chemotherapy, or radiation. We describe the case of a 45-year-old gentleman with primary cardiac synovial sarcoma of the heart, metastasizing to the lung. The tumor was resected, and the patient underwent chemotherapy with regression of the lung nodules.