EEG – Imaging Evolution of the MV2 Subtype of Sporadic Creutzfeldt-Jakob Disease During the two-Year Course of the Disease-Reference-Cited by-同舟云学术

EEG – Imaging Evolution of the MV2 Subtype of Sporadic Creutzfeldt-Jakob Disease During the two-Year Course of the Disease

Published:2022-05-18 Issue:2 Volume:54 Page:164-167
ISSN:1550-0594
Container-title:Clinical EEG and Neuroscience
language:en
Short-container-title:Clin EEG Neurosci

Author:

Theodora Afrantou¹^ORCID,Styliani-Aggeliki Syntila¹,Panagiotis Ioannidis¹,Theodoros Sklaviadis²,Marina Boziki¹,Nikolaos Grigoriadis¹

Affiliation:

1. 2nd Department of Neurology, AHEPA University Hospital, Aristotle University of Thessaloniki, Thessaloniki, Greece

2. Laboratory of Pharmacology, School of Health Sciences, Department of Pharmacy, Aristotle University of Thessaloniki, Thessaloniki, Greece

Abstract

Sporadic Creutzfeldt–Jakob disease (sCJD) is a rare transmissible disease. According to molecular classification, six clinical phenotypes of sCJD have been described: MM1, MM2, MV1, MV2, VV1 and VV2. MV2 subtype comprises 9% of sCJD cases. Atypical clinical course has been reported to be the main caveat for the diagnosis of the MV2 subtype. We hereby present a rare case of MV2 subtype of sCJD, highlighting the evolution of clinical, EEG and imaging attributes over a two-year period, thus underlining the atypical course of the disease.

Publisher

SAGE Publications

Subject

Neurology (clinical),Neurology,General Medicine

Link

http://journals.sagepub.com/doi/pdf/10.1177/15500594221101628

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