Intractable Epilepsy With Ring Chromosome 20 Syndrome Treated With Vagal Nerve Stimulation: Case Report and Review of the Literature

Author:

Chawla Jasvinder1,Sucholeiki Roy2,Jones Carolyn3,Silver Kenneth4

Affiliation:

1. Department of Neurology Loyola University Medical Center Maywood, Illinois,

2. Department of Neurology Loyola University Medical Center Maywood, Illinois

3. Department of Pediatrics and Genetics Loyola University Medical Center Maywood, Illinois

4. Department of Neurology University of Chicago Children's Hospital Chicago, Illinois

Abstract

We report a case of a 6-year old girl with ring chromosome 20 syndrome whose medically intractable seizures were successfully treated with vagal nerve stimulation therapy. Medically intractable seizures are an expected part of this rare syndrome, and the dramatic improvement in seizure control with vagal nerve stimulation is emphasized. Earlier use of vagal nerve stimulation in similar cases should be considered. ( J Child Neurol 2002;17:778—780).

Publisher

SAGE Publications

Subject

Clinical Neurology,Pediatrics, Perinatology, and Child Health

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