Childhood Orbital Pseudotumor: Case Report and Literature Review

Author:

Kitei Dan1,DiMario Francis J.2

Affiliation:

1. Department of Neurology, University of Connecticut School of Medicine, Connecticut Children's Medical Center, Hartford, CT

2. Department of Neurology, University of Connecticut School of Medicine, , Department of Pediatrics University of Connecticut School of Medicine, Farmington, Connecticut Children's Medical Center, Hartford, CT

Abstract

Orbital pseudotumor, also known as idiopathic orbital inflammation, is a benign, idiopathic, noninfectious, and nonneoplastic clinical syndrome with an inflammatory mass within the orbit and no identifiable cause. This disease is rare in the pediatric population, especially in very young children. In this article, the authors describe a 2-year-old girl who was presented with right eye ptosis, near-complete ophthalmoplegia, decreased visual acuity, and pupillary changes. She recovered completely with high-dose steroid therapy. The authors review the literature and discuss the diagnostic implications and treatment strategies.

Publisher

SAGE Publications

Subject

Clinical Neurology,Pediatrics, Perinatology, and Child Health

Cited by 38 articles. 订阅此论文施引文献 订阅此论文施引文献,注册后可以免费订阅5篇论文的施引文献,订阅后可以查看论文全部施引文献

1. Limited granulomatosis with polyangiitis in children with idiopathic orbital inflammation: a case series and literature review;Rheumatology International;2023-06-15

2. Orbital pseudotumor in pediatrics: A single tertiary center experience;Clinical Case Reports;2023-03

3. The clinical presentation and magnetic resonance imaging characteristics of an infant with idiopathic orbital inflammation;Journal of American Association for Pediatric Ophthalmology and Strabismus;2022-04

4. Orbital inflammatory disease;Archivos de la Sociedad Española de Oftalmología (English Edition);2022-02

5. Enfermedad inflamatoria orbitaria idiopática;Archivos de la Sociedad Española de Oftalmología;2022-02

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