Type A4 Truncus Arteriosus with Quadricuspid Truncal Valve: A Rare Cause of Infantile Heart Failure

Abstract

Truncus arteriosus is an exceedingly rare congenital heart disease involving the conotruncal septum of the developing heart. Clinical presentations vary depending on associated anomalies. Surgical management is extremely challenging and differs with anatomic subtypes. We present a case of truncus arteriosus––Vaan Praagh type A4, quadricuspid truncal valve with moderate truncal stenosis and regurgitation, type B interrupted aortic arch who underwent bilateral pulmonary artery banding.