Giant Right Ventricular Fibroma: Prenatal Diagnosis and Partial Resection in Early Infancy

Author:

Juaneda Ignacio1ORCID,Bueno Nora23,Ochoa Jose2,Díaz Juan3,Peirone Alejandro4

Affiliation:

1. Division of Congenital Heart Surgery, Hospital Privado Universitario de Córdoba, Argentina

2. Division of Fetal Diagnosis, Diagnus, Centro Médico de Diagnóstico Especializado, Córdoba, Argentina

3. Division of Cardiac Intensive Care Unit, Hospital Privado Universitario de Córdoba, Argentina

4. Division of Pediatric Cardiology, Hospital Privado Universitario de Córdoba, Argentina

Abstract

Congenital cardiac fibromas are very rare and prenatal diagnosis has been reported in just a few cases. We describe a four-month-old infant presenting a symptomatic giant right ventricular fibroma discovered during prenatal scanning at 33 weeks of gestation, which was confirmed after delivery on echocardiogram and cardiac magnetic resonance imaging. Due to progressive hemodynamic deterioration, partial surgical resection was performed and the patient recovered uneventfully. We report the successful management during early infancy of a giant cardiac fibroma prenatally diagnosed.

Publisher

SAGE Publications

Subject

Cardiology and Cardiovascular Medicine,General Medicine,Pediatrics, Perinatology and Child Health,Surgery

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