Abstract
Objective: possibility of surgical treatment of chest deformity in children with Jeune syndrome (analysis of the clinical case), review of literature on Jeune syndrome in children.
Methods: clinical, radiological, laboratory, instrumental, statistical.
Results: Positive outcome of surgical treatment of a 3-year-old patient with severe chest deformity and severe respiratory failure.
Conclusions: Jeune syndrome is a severe disease with a high mortality rate. A multidisciplinary approach is required in the treatment of patients with this pathology. Surgical intervention aimed at reducing the compression of the chest organs and increasing its volume, even in conditions of decompensation, allows you to stop the phenomenon of respiratory failure.