A CLN6-CLN8 complex recruits lysosomal enzymes at the ER for Golgi transfer
Author:
Funder
National Institutes of Health; Gwenyth Gray Foundation; Beyond Batten Disease Foundation; NCL-Stiftung; CPRIT
Publisher
American Society for Clinical Investigation
Subject
General Medicine
Link
https://www.jci.org/articles/view/130955/files/pdf
Reference81 articles.
1. The endosomal-lysosomal system: from acidification and cargo sorting to neurodegeneration;Hu;Transl Neurodegener,2015
2. Lysosome biogenesis in health and disease
3. Lysosomal hydrolase mannose 6-phosphate uncovering enzyme resides in the trans-Golgi network;Rohrer;Mol Biol Cell,2001
4. CLN8 is an endoplasmic reticulum cargo receptor that regulates lysosome biogenesis
5. The neuronal ceroid lipofuscinosis CLN8 membrane protein is a resident of the endoplasmic reticulum
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