Affiliation:
1. Jennifer Hodnett, Marcus Autism Center, Atlanta, GA; Mindy Scheithauer, Nathan A. Call, Joanna Lomas Mevers, and Sarah J. Miller, Marcus Autism Center; Emory University School of Medicine; Atlanta, GA.
Abstract
Abstract
Smith-Magenis syndrome (SMS) is a genetic disorder, commonly caused by a 17p11.2 deletion, affecting the Retinoic Acid Induced 1 gene. It affects approximately 1 in 25,000 individuals, with over 90% engaging in challenging behaviors. Function-based treatments, using the principles of applied behavior analysis, have consistently been shown to decrease challenging behaviors exhibited by individuals with developmental delays. However, additional research is needed to determine the effects of these interventions with specific diagnostic subsets, including SMS. The current study identified the function of challenging behavior for 2 children with SMS and found a function-based treatment, consisting of differential reinforcement and extinction, reduced challenging behavior for both.
Publisher
American Association on Intellectual and Developmental Disabilities (AAIDD)
Subject
Psychiatry and Mental health,Neurology (clinical),Arts and Humanities (miscellaneous),Developmental and Educational Psychology,Neuropsychology and Physiological Psychology,General Medicine,Pediatrics, Perinatology and Child Health
Cited by
6 articles.
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1. Behavioural phenotype of SYNGAP1‐related intellectual disability;Journal of Intellectual Disability Research;2024-05-23
2. Research on Challenging Behaviors and Functional Assessment;Functional Assessment for Challenging Behaviors and Mental Health Disorders;2021
3. Populations and Problems Evaluated with Functional Assessment;Functional Assessment for Challenging Behaviors and Mental Health Disorders;2021
4. SMITH–MAGENIS SYNDROME;Cassidy and Allanson's Management of Genetic Syndromes;2020-10-30
5. Prevalence of renewal of problem behavior during context changes;Journal of Applied Behavior Analysis;2020-01-07