Monogenic autoinflammatory syndromes with features of systemic vasculitis: a new field of rheumatology-Reference-Cited by-同舟云学术

Monogenic autoinflammatory syndromes with features of systemic vasculitis: a new field of rheumatology

Published:2023-08-31 Issue:4 Volume:61 Page:458-465
ISSN:1995-4492
Container-title:Rheumatology Science and Practice
language:
Short-container-title:Naučno-praktičeskaâ revmatologiâ

Author:

Beketova T. V.¹^ORCID,Beketova M. F.²^ORCID,Nasonov E. L.³^ORCID

Affiliation:

1. Central State Medical Academy of the Administrative Directorate of the President of the Russian Federation; V.A. Nasonova Research Institute of Rheumatology; Moscow Polytechnic University

2. Lomonosov Moscow State University

3. V.A. Nasonova Research Institute of Rheumatology; I.M. Sechenov First Moscow State Medical University of the Ministry of Health Care of Russian Federation (Sechenov University)

Abstract

The article is dedicated to a new actual problem in rheumatology: vasculitis and vasculitis-like manifestations in monogenic autoinflammatory syndromes in adult. The features of the clinical course of the rarely diagnosed VEXAS syndrome, as well as the SAVI and COPA syndromes, which sometimes occur in adults, are considered. Promising directions of future treatment are discussed.

Publisher

Mediar Press

Subject

Immunology,Immunology and Allergy,Rheumatology

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