Effect of Carnitine Administration on Glycine Metabolism in Patients with Isovaleric Acidemia: Significance of Acetylcarnitine Determination to Estimate the Proper Carnitine Dose.-Reference-Cited by-同舟云学术

Effect of Carnitine Administration on Glycine Metabolism in Patients with Isovaleric Acidemia: Significance of Acetylcarnitine Determination to Estimate the Proper Carnitine Dose.

Published:1996 Issue:2 Volume:179 Page:101-109
ISSN:0040-8727
Container-title:The Tohoku Journal of Experimental Medicine
language:en
Short-container-title:Tohoku J. Exp. Med.

Author:

Itoh Tamiko¹,Ito Tetsuya²,Ohba Satoru²,Sugiyama Naruji²,Mizuguchi Kouhei³,Yamaguchi Seiji⁴,Kidouchi Kiyoshi⁵

Affiliation:

1. Department of Pediatrics, Nagoya City Midori Municipal Hospital

2. Nagoya City University Medical School

3. Takayama Red Cross Hospital

4. Shimane Medical University

5. Nagoya City Higashi General Hospital

Publisher

Tohoku University Medical Press

Subject

General Biochemistry, Genetics and Molecular Biology,General Medicine

Link

http://www.jstage.jst.go.jp/article/tjem/179/2/179_2_101/_pdf

Reference18 articles.

1. Isovaleric acidemia: Medical and neurodevelopmental effects of long-term therapy

2. Secondary carnitine insufficiency in disorders of organic acid metabolism: modulation of acyl-CoA/CoA ratios by l-carnitine in vivo

3. The response to l-carnitine and glycine therapy in isovaleric acidaemia

4. Acute and Chronic-Intermittent Isovaleric Acidemia: Diagnosis and Glycine Therapy

5. Analytical method for urinary glutarylcarnitine, acetylcarnitine and propionylcarnitine with a carboxylic acid analyser and a reversed-phase column

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