Dysregulation of C/EBPα by mutant Huntingtin causes the urea cycle deficiency in Huntington's disease-Reference-Cited by-同舟云学术

Dysregulation of C/EBPα by mutant Huntingtin causes the urea cycle deficiency in Huntington's disease

Published:2007-01-09 Issue:5 Volume:16 Page:483-498
ISSN:1460-2083
Container-title:Human Molecular Genetics
language:en
Short-container-title:

Author:

Chiang Ming-Chang,Chen Hui-Mei,Lee Yi-Hsin,Chang Hao-Hung,Wu Yi-Chih,Soong Bing-Wen,Chen Chiung-Mei,Wu Yih-Ru,Liu Chin-San,Niu Dau-Ming,Wu Jer-Yuarn,Chen Yuan-Tsong,Chern Yijuang

Publisher

Oxford University Press (OUP)

Subject

Genetics (clinical),Genetics,Molecular Biology,General Medicine

Link

http://academic.oup.com/hmg/article-pdf/16/5/483/2085245/ddl481.pdf

Reference66 articles.

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2. Differential loss of striatal projection neurons in Huntington disease;Reiner;PNAS,1988

3. Length of huntingtin and its polyglutamine tract influences localization and frequency of intracellular aggregates;Martindale;Nat. Genet.,1998

4. cAMP-response element-binding protein contributes to suppression of the A2A adenosine receptor promoter by mutant Huntingtin with expanded polyglutamine residues;Chiang;J. Biol. Chem.,2005

5. The Huntington's disease protein interacts with p53 and CREB-binding protein and represses transcription;Steffan;Proc. Natl Acad. Sci. USA,2000

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