Pantethine treatment is effective in recovering the disease phenotype induced by ketogenic diet in a pantothenate kinase-associated neurodegeneration mouse model-Reference-Cited by-同舟云学术

Pantethine treatment is effective in recovering the disease phenotype induced by ketogenic diet in a pantothenate kinase-associated neurodegeneration mouse model

Published:2013-12-06 Issue:1 Volume:137 Page:57-68
ISSN:1460-2156
Container-title:Brain
language:en
Short-container-title:

Author:

Brunetti Dario,Dusi Sabrina,Giordano Carla,Lamperti Costanza,Morbin Michela,Fugnanesi Valeria,Marchet Silvia,Fagiolari Gigliola,Sibon Ody,Moggio Maurizio,d’Amati Giulia,Tiranti Valeria

Publisher

Oxford University Press (OUP)

Subject

Neurology (clinical)

Link

http://academic.oup.com/brain/article-pdf/137/1/57/13797126/awt325.pdf

Reference40 articles.

1. Cystamine and cysteamine increase brain levels of BDNF in Huntington disease via HSJ1b and transglutaminase;Borrell-Pages;J Clin Invest,2006

2. Is taurine a functional nutrient?;Bouckenooghe;Curr Opin Clin Nutr Metab Care,2006

3. Cystamine metabolism and brain transport properties: clinical implications for neurodegenerative diseases;Bousquet;J Neurochem,2010

4. Pantothenate kinase-associated neurodegeneration: altered mitochondria membrane potential and defective respiration in Pank2 knock-out mouse model;Brunetti;Hum Mol Genet,2012

5. Adverse reactions to oral cysteamine use in nephropathic cystinosis;Corden;Dev Pharmacol Ther,1981

Cited by 79 articles. 订阅此论文施引文献订阅此论文施引文献，注册后可以免费订阅5篇论文的施引文献，订阅后可以查看论文全部施引文献

1. Pantethine ameliorates dilated cardiomyopathy features in PPCS deficiency disorder: evidence from patients and models of the disease;2024-08-22

2. Mitochondrial iron deficiency triggers cytosolic iron overload in PKAN hiPS-derived astrocytes;Cell Death & Disease;2024-05-25

3. Non-Targeted Metabolomics Reveals the Metabolic Alterations in Response to Artificial Selective Breeding in the Fast-Growing Strains of Pacific Oyster;Journal of Ocean University of China;2024-04

4. Patient-Derived Cellular Models for Polytarget Precision Medicine in Pantothenate Kinase-Associated Neurodegeneration;Pharmaceuticals;2023-09-26

5. Advances in Mitochondria-Targeted Drug Delivery;Pharmaceutics;2023-08-05