Decreased serum ubiquinone-10 concentrations in phenylketonuria
Author:
Affiliation:
1. From the Servei de Bioquímica, Servei de Pediatría i Neuropediatría, Unitat Integrada, Hospital Sant Joan de Déu/Hospital Clinic, Universitat de Barcelona, Spain.
Publisher
Oxford University Press (OUP)
Subject
Nutrition and Dietetics,Medicine (miscellaneous)
Link
http://academic.oup.com/ajcn/article-pdf/70/5/892/23937967/892.pdf
Reference20 articles.
1. The hyperphenylalaninemias;Scriver,1995
2. Large daily fluctuations in plasma tyrosine in treated patients with phenylketonuria;van Spronsen;Am J Clin Nutr,1996
3. Nutrient intakes of adolescents with phenylketonuria and infants and children with maple syrup urine disease on semisynthetic diets;Gropper;J Am Coll Nutr,1993
4. Controlled diet in phenylketonuria may cause serum carnitine deficiency;Vilaseca;J Inherit Metab Dis,1993
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