Odontogenic fibroma-like lesions associated with amelogenesis imperfecta: short case

Abstract

Observation: We present a case of a 21-year-old Pakistani female with hypoplastic amelogenesis imperfecta (AI), microdontia, and multiple gingival swellings overlying impacted teeth. The gingival swellings were diagnosed as AI-associated odontogenic fibroma (OF)-like lesions on histology. Commentary: AI is an inherited enamel defect that may present in association with microdontia, root abnormalities, taurodontism, pulp stones, gingival hyperplasia, and rarely, gingival tumors. These gingival tumors share histologic features with odontogenic fibroma (OF), a benign odontogenic neoplasm, and are referred to as AI-associated OF-like lesions in the literature. Conclusion: AI-associated OF-like lesions are rare, this case will inform oral surgeons and other dental practitioners about this process and its management.