A case of inherited metabolic disorder with airway difficulties in intensive care- challenges faced

Abstract

Uncommon disease like MPS imposes great challenges to intensivists in case of emergency due to their disease nature which involves GAG accumulation leading to cellular dysfunction and various clinical abnormalities. Airway management in Pediatric patients is extremely demanding even with expert hands. So, this case report discusses mainly the disease progress, and anticipated anesthetic challenges with its skillful handling strategy that has to be contemplated in case of emergency situation. Keywords: intensive care, cellular dysfunction, clinical abnormalities