1. deficiency of PDHC reviewed was hyperuricemia. polypeptide of mammalian pyruvate dehydrogenase complex Since thiamine pyrophosphate is an integral component participates in acetylation reactions. Eur J Biochem 1986; 158:
2. described as thiamine-dependent [25]. In other patients, a complex and function of protein X. J Biol Chem 1989; 264:
3. dramatic improvements in some patients with PDH oxidation and the conservation of glucose. Biochem Soc Symp