Effect of retinol dehydrogenase gene transfer in a novel rat model of Stargardt disease
Author:
Affiliation:
1. Université de NantesCHU de Nantes, INSERM UMR 1089, Translational Gene Therapy for Genetic Diseases Nantes France
2. Inserm UMR1280 Nantes France
3. Department of Ophthalmology University Hospital of NantesCHU de Nantes Nantes France
Publisher
Wiley
Subject
Genetics,Molecular Biology,Biochemistry,Biotechnology
Link
https://onlinelibrary.wiley.com/doi/pdf/10.1096/fj.202002525RRR
Reference58 articles.
1. N-Retinylidene-phosphatidylethanolamine Is the Preferred Retinoid Substrate for the Photoreceptor-specific ABC Transporter ABCA4 (ABCR)
2. Interaction of the Nucleotide Binding Domains and Regulation of the ATPase Activity of the Human Retina Specific ABC Transporter, ABCR
3. Retinal Stimulates ATP Hydrolysis by Purified and Reconstituted ABCR, the Photoreceptor-specific ATP-binding Cassette Transporter Responsible for Stargardt Disease
4. A photoreceptor cell-specific ATP-binding transporter gene (ABCR) is mutated in recessive Starqardt macular dystrophy
5. Organization of the ABCR gene: analysis of promoter and splice junction sequences;Allikmets R;Gene,1998
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