Gorlin–Goltz Syndrome: Report of Two Cases

Abstract

ABSTRACT Gorlin–Goltz syndrome is an uncommon autosomal dominant inherited disorder with complete penetrance and extreme variable expressivity. It is characterized by multiple odontogenic keratocysts and basal cell carcinomas; skeletal, dental, ophthalmic, and neurological abnormalities; intracranial ectopic calcifications of the falx cerebri, and facial dysmorphism. Due to importance of oral maxillofacial manifestations of this syndrome, it is important to know its characteristics in order to make diagnosis and to provide an early preventive treatment. The purpose of this article is to present a report of two cases who reported to the Department of Oral and Maxillofacial Surgery, with features of Gorlin–Goltz syndrome in association with multiple odontogenic keratocysts in the maxillofacial region. How to cite this article Bharti R, Jindal G, Garg S, Kaur S, Goyal M, Gupta P. Gorlin–Goltz Syndrome: Report of Two Cases. Int J Clin Dent Res 2017;1(1):49-54.